@article{uoadl:3107311, volume = "23", number = "4", journal = "Annals of Noninvasive Electrocardiology", issn = "1082-720X, 1542-474X", keywords = "amiodarone; dihydroquinidine; isoprenaline; metoprolol; quinidine, acute heart infarction; adult; Article; case report; catheter ablation; clinical article; dizziness; early repolarization syndrome; early repolarization syndrome; electrocardiogram; faintness; female; heart muscle conduction disturbance; heart ventricle extrasystole; heart ventricle fibrillation; human; implantation; polymorphic ventricular tachycardia; priority journal; repetitive incessant electrical storm; repetitive incessant electrical storm; ST segment elevation; visual disorder; complication; electrocardiography; heart ventricle fibrillation; heart ventricle tachycardia; implantable cardioverter defibrillator; procedures; recurrent disease, Adult; Catheter Ablation; Defibrillators, Implantable; Electrocardiography; Female; Humans; Recurrence; Tachycardia, Ventricular; Ventricular Fibrillation", BIBTEX_ENTRY = "article", year = "2018", author = "Chatzidou, S. and Repasos, E. and Plastiras, S. and Kontogiannis, C. and Kosmopoulos, M. and Tsilimigras, D.I. and Paraskevaidis, I. and Rokas, S.", abstract = "Early repolarization syndrome (ERS) was originally considered a normal variant with benign outcome. However, recent studies have demonstrated that it can be linked to a considerable risk of life-threatening arrhythmias and sudden cardiac death. We report a case with an extraordinary, extremely malignant clinical expression of ERS refractory to all antiarrhythmic drugs including quinidine. This case demonstrates real-time changes of dynamic electrocardiogram (ECG) preceding a polymorphic ventricular tachycardia (VT)-ventricular fibrillation (VF) and possible external factors triggering arrhythmia onset. Implantable cardioverter-defibrillator (ICD) function was terminated 6 months after implantation due to multiple-incessant electrical storm (ES). Catheter ablation was the definite treatment of this malignant entity. © 2017 Wiley Periodicals, Inc.", title = "Repetitive-incessant electrical storm triggered by early repolarization", doi = "10.1111/ANEC.12518" }