TY - JOUR
TI - Fixed subaortic stenosis revisited - Congenital abnormalities in 72 new
cases and review of the literature
AU - Tentolouris, K
AU - Kontozoglou, T
AU - Trikas, A
AU - Brilli, S and
AU - Chlapoutakis, E
AU - Exadactylos, N
AU - Pitsavos, C
AU - Toutouzas, P
JO - European Cardiology Review
PY - 1999
VL - 92
TODO - 1
SP - 4-10
PB - Karger
SN - null
TODO - 10.1159/000006939
TODO - congenital heart disease; congenital abnormalities; aortic stenosis
TODO - Seventy-two patients aged 2-65 years (mean 20.2) with fixed subaortic
stenosis (FSS) are reported. All patients underwent echocardiography and
angiography prior to surgical intervention, Sixty-four (89%) had
discrete subaortic stenosis (DSS) and 8 (11%) tunnel type stenosis
(TSS). Patients with DSS aged 2-65 years (mean 29) while patients with
TSS aged 10-34 years (mean 19) and had a distinct female preponderance
(7:1). Twenty-five patients (39%) with DSS had other congenital
abnormalities of which aortic stenosis associated with bicuspid aortic
valve was slightly more common than ventricular septal defect (7:6),
Five patients with TSS had a small aortic annulus and hypoplastic aorta.
Our data and those in the literature indicate that TSS although related
to DSS has certain features that may set it apart as a distinct entity.
In addition DSS appears to be associated with aortic stenosis and
bicuspid aortic valve as frequently as with ventricular septal defect.
Copyright (C) 2000 S. Karger AG, Basel.
ER -