TY - JOUR
TI - Unstable angina associated with coronary arterial calcification in a
thalassemia intermedia patient with a pseudoxanthoma elasticum-like
syndrome
AU - Farmakis, D
AU - Moyssakis, I
AU - Perakis, A
AU - Rombos, Y
AU - Deftereos,
AU - S
AU - Giakoumis, A
AU - Polymeropoulos, E
AU - Aessopos, A
JO - European Journal of Haematology
PY - 2003
VL - 70
TODO - 1
SP - 64-66
PB - Wiley
SN - 0902-4441, 1600-0609
TODO - 10.1034/j.1600-0609.2003.02864.x
TODO - thalassemia; pseudoxanthoma elasticum; coronary artery disease; arterial
calcification
TODO - The coexistence of a pseudoxanthoma elasticum (PXE)-like syndrome in
beta-thalassemia and other hemoglobinopathies is a recently established
clinical entity that has been observed with a significant frequency and
related to some severe, even life-threatening complications. We present
here a thalassemia intermedia patient who developed unstable angina in a
setting of severe anemia and PXE-related coronary arterial
calcification. Besides the clinical significance of this PXE-like
syndrome, its acquired nature may introduce some new thoughts regarding
the pathogenesis of atherosclerosis.
ER -