TY - JOUR
TI - Safety and efficacy of pirfenidone and nintedanib in patients with idiopathic pulmonary fibrosis and carrying a telomere-related gene mutation
AU - Justet, A.
AU - Klay, D.
AU - Porcher, R.
AU - Cottin, V.
AU - Ahmad, K.
AU - Molina, M.M.
AU - Nunes, H.
AU - Reynaud-Gaubert, M.
AU - Naccache, J.M.
AU - Manali, E.
AU - Froidure, A.
AU - Jouneau, S.
AU - Wemeau, L.
AU - Andrejak, C.
AU - Gondouin, A.
AU - Hirschi, S.
AU - Blanchard, E.
AU - Bondue1, B.
AU - Bonniaud, P.
AU - Tromeur, C.
AU - Prévot, G.
AU - Marchand-Adam, S.
AU - Funke-Chambour, M.
AU - Gamez, A.S.
AU - Ba, I.
AU - Papiris, S.
AU - Grutters, J.
AU - Crestani, B.
AU - Van Moorsel, C.
AU - Kannengiesser, C.
JO - European Respiratory Journal
PY - 2021
VL - 57
TODO - 2
SP - null
PB - European Respiratory Society
SN - 0903-1936, 1399-3003
TODO - 10.1183/13993003.03198-2020
TODO - dyskerin;  nintedanib;  pirfenidone;  telomerase reverse transcriptase;  dipyrone;  indole derivative;  nintedanib;  pirfenidone, age;  antifibrotic therapy;  Belgium;  confounding variable;  demography;  diffusing capacity for carbon monoxide;  disease exacerbation;  disease severity;  drug efficacy;  drug safety;  drug withdrawal;  fibrosing alveolitis;  follow up;  forced vital capacity;  gastrointestinal disease;  gene;  gene mutation;  genetic variability;  Greece;  human;  hypertransaminasemia;  Letter;  lung fibrosis;  lung function test;  lung transplantation;  multidisciplinary team;  Netherlands;  PARN gene;  people by smoking status;  prediction;  respiratory failure;  RTEL1 gene;  self report;  skin manifestation;  Spain;  Switzerland;  telomere;  TERC gene;  TERT gene;  treatment withdrawal;  fibrosing alveolitis;  genetics;  mutation;  treatment outcome, Humans;  Idiopathic Pulmonary Fibrosis;  Indoles;  Mutation;  Pyridones;  Telomere;  Treatment Outcome
TODO - null
ER -