TY - JOUR
TI - Pseudomyxoma Peritonei: Presentation of Two Cases and Challenging Issues
in the Literature
AU - Pantiora, Eirini V.
AU - Massaras, Dimitrios
AU - Koutalas, John and
AU - Melemeni, Aikaterini
AU - Fragulidis, Georgios P.
JO - CUREUS
PY - 2018
VL - 10
TODO - 12
SP - null
PB - CUREUS INC
SN - null
TODO - 10.7759/cureus.3732
TODO - pseudomyxoma peritonei; cytoreductive surgery; intraperitoneal
hyperthennia; appendiceal neoplasm; classification; hipec
TODO - Pseudomyxoma peritonei (PMP) is a rather uncommon syndrome in oncology
with a unique biological behavior and an estimated incidence of one to
two cases per million per year. Clinically, it usually presents with a
variety of unspecific signs and symptoms including abdominal pain and
distention, ascites, or even bowel obstruction. Despite its intimidating
clinical manifestation, PMP is characterized by satisfactory survival
rates when treated with cytoreduction and hyperthermic intraperitoneal
chemotherapy (HIPEC).
We present two interesting cases of PMP deriving from the appendix with
a rather atypical presentation, which was successfully treated with
cytoreduction and HIPEC. In addition, we intend to raise clinical
suspicion on the diagnosis of PMP and comment on several challenging
issues concerning the origin and classification of PMP.
ER -