Τίτλος:
Primary hemangiopericytoma arising in extralobar pulmonary sequestration: A coincidence or two rare disorders?
Γλώσσες Τεκμηρίου:
Αγγλικά
Περίληψη:
Background/Aim: Extralobar pulmonary sequestration (EPS) is an unusual congenital defect characterized by the presence of non-functioning lung tissue receiving arterial supply from the systemic arteries. Primary hemangiopericytoma (HPC) is an uncommon potentially malignant tumor of vascular origin that usually involves the soft tissue of the extremities or retroperitoneum, but extremely rarely affects the lung. We present the rare case of a primary pulmonary HPC arising in an EPS. Case Report: A 65-year-old woman, with dyspnea and pleuritic chest pain, was referred for further investigation. Radiological evaluation demonstrated a well-circumscribed mass above the right hemidiaphragm, receiving its arterial supply from the descending thoracic aorta. The patient underwent a right posterolateral thoracotomy and a middle lobectomy. The intraoperative finding was a well-encapsulated solid mass. The histological evaluation described HPC. Results: The patient remains fit and healthy. Conclusion: Pulmonary HPC can arise in EPS. Surgical excision is the treatment of choice. © 2019 International Institute of Anticancer Research. All rights reserved.
Συγγραφείς:
Kampolis, C.F.
Damaskos, C.
Loukeri, A.A.
Garmpis, N.
Garmpi, A.
Tomos, I.
Spartalis, E.
Dimitroulis, D.
Patsouras, A.
Douskou, M.
Papiris, S.A.
Tomos, P.
Περιοδικό:
In vivo (Athens, Greece)
Εκδότης:
International Institute of Anticancer Research
Λέξεις-κλειδιά:
aged; arterial circulation; Article; case report; clinical article; computed tomographic angiography; dyspnea; female; hemangiopericytoma; hemidiaphragm; human; human tissue; lobectomy; lung sequestration; multidetector computed tomography; pleura effusion; thoracic aorta; thoracotomy; thorax pain; tumor recurrence; biopsy; complication; differential diagnosis; hemangiopericytoma; lung sequestration; symptom assessment; treatment outcome; x-ray computed tomography, biological marker, Aged; Biomarkers; Biopsy; Bronchopulmonary Sequestration; Diagnosis, Differential; Female; Hemangiopericytoma; Humans; Symptom Assessment; Tomography, X-Ray Computed; Treatment Outcome
DOI:
10.21873/invivo.11715
