Τίτλος:
Unstable angina associated with coronary arterial calcification in a
thalassemia intermedia patient with a pseudoxanthoma elasticum-like
syndrome
Γλώσσες Τεκμηρίου:
Αγγλικά
Περίληψη:
The coexistence of a pseudoxanthoma elasticum (PXE)-like syndrome in
beta-thalassemia and other hemoglobinopathies is a recently established
clinical entity that has been observed with a significant frequency and
related to some severe, even life-threatening complications. We present
here a thalassemia intermedia patient who developed unstable angina in a
setting of severe anemia and PXE-related coronary arterial
calcification. Besides the clinical significance of this PXE-like
syndrome, its acquired nature may introduce some new thoughts regarding
the pathogenesis of atherosclerosis.
Συγγραφείς:
Farmakis, D
Moyssakis, I
Perakis, A
Rombos, Y
Deftereos,
S
Giakoumis, A
Polymeropoulos, E
Aessopos, A
Περιοδικό:
European Journal of Haematology
Λέξεις-κλειδιά:
thalassemia; pseudoxanthoma elasticum; coronary artery disease; arterial
calcification
DOI:
10.1034/j.1600-0609.2003.02864.x
